A fatal case of Degos’ disease which presented with recurrent intestinal perforation
نویسندگان
چکیده
منابع مشابه
Dowling-Degos disease: Report of a case with pigmentation localized only in the genital area
Dowling –Degos disease is a rare condition. It is inherited by an autosomal dominant gene. It usually presents in adult life as small, pigmented, asymptomatic macules in flexural regions. We report a 35-year-old woman with Dowling- Degos disease, in whom the reticular pigmentation confined to the genital area.
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Dowling-Degos disease (DDD) or reticular pigmented anomaly of the flexures is a rare autosomal dominant genodermatosis with variable penetrance. It mainly affects young women and is characterized by acquired reticular hyperpigmentation of the large skin folds. We present a case of DDD associated with hidradenitis suppurativa (HS) in a 43-year-old Spanish woman. Physical examination revealed bro...
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A 45-year-old woman was admitted to our emergency service with nausea and severe abdominal pain which started five days ago. She had 6 weeks of pregnancy and four years ago was diagnosed with Behçet's disease (BD) with oral, ocular and genital involvement. She had been taking colchicine 3 mg/day since from the diagnosis. At physical examination oral aphthous ulcerations, extensive abdominal ten...
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Case report The patient was a 35-year-old housewife who developed Raynaud's phenomenon in 1965. Two years later, when she was admitted into hospital for treatment of broncho-pneumonia, early changes of scleroderma were noted in the hands and face. In May 1969 she developed severe proximal muscle weakness and it was found that the skin changes had considerably extended to involve the hands, fore...
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ژورنال
عنوان ژورنال: World Journal of Gastrointestinal Surgery
سال: 2011
ISSN: 1948-9366
DOI: 10.4240/wjgs.v3.i10.156